Surgical Outcomes of Repairing Ebstein Anomaly: A Single-Center Experience

Background: Ebstein anomaly (EA) is a rare congenital disorder of the tricuspid valve (TV), accounting for about one percent heart defects. Considering highly variable anatomy, diverse corrective surgical methods are currently utilized. Cone reconstruction provides near anatomic restoration method that has triggered enthusiasm early repair over recent years. Objectives: In current study, we aimed to evaluate clinical and echocardiographic features outcomes patients who underwent correction EA in our referral center. Methods: this reviewed medical records 35 with cone or TV replacement had accessible data before at least year following surgery. The were evaluated residual regurgitation (TR) severity, right ventricular (RV) size, RV fractional area change (FAC), left end-systolic diameter (LVESD), end-diastolic (LVEDD), 2D ejection fraction (LVEF) after operation. Results: Mean age was 29.49 ± 9.13 years, 54.3% them female. Twenty-one (60%) repair, 14 subjected replacement. Seven (20%) required reoperation; redo conducted three (8.6%); two (5.7%) biologic replacement; mechanical performed patient (2.9%) degenerative TVs, redo-operation due malfunction. Positive changes means RV-FAC 2D-LVEF statistically significant all irrespective type surgery (P < 0.001), but size = 0.38) LVESD 0.302) not significant. There increase functional both groups 0.063) 0.02). Conclusions: present study revealed satisfactory post-op results EA, evidenced by reduced TR severity improved biventricular parameters. Assessing durability needs longer-term follow-ups.